About MBD4
No gene-level summary was recorded for this case.
No variant summary was recorded for this case.
Five-step scale from benign to pathogenic. This variant is benign. Select a step to read what it means.
Benign.A benign classification under the recorded framework.
Gene-level background from the recorded interpretation.
Words with a dotted underline have a short definition. Hover or tap them.No gene-level summary was recorded for this case.
The recorded framework is Not recorded. The criteria and strengths shown below come from the saved assessment; this page does not recalculate the classification.
The applied criteria and their strengths are shown as assessed under the stated framework.
No pathogenic criterion marked as applied in the recorded assessment.
This variant is present at extremely high allele frequency in population databases, far exceeding the BA1 threshold of >1%. gnomAD v2.1: AF=7.89% (22,303/282,770 alleles, 999 homozygotes). gnomAD v4.1: AF=8.41% (135,695/1,614,010 alleles, 6,177 homozygotes). Highest subpopulation frequency in Ashkenazi Jewish: 16.24% (v2.1) / 16.28% (v4.1). The presence of 999–6,177 homozygotes across gnomAD datasets definitively establishes this as a common benign polymorphism.
Allele frequency far exceeds the BS1 threshold of >0.3%. gnomAD v2.1 AF=7.89% and gnomAD v4.1 AF=8.41% both vastly surpass the 0.3% cutoff. While BA1 (stand-alone benign) supersedes this criterion, the population data independently satisfies BS1 at strong benign strength.
Observed in 999 homozygous individuals in gnomAD v2.1 and 6,177 homozygous individuals in gnomAD v4.1, definitively confirming observation in healthy adults. For MBD4-associated cancer predisposition syndromes (colorectal oligopolyposis, melanoma), this number of homozygotes is incompatible with a highly penetrant pathogenic role.
Multiple lines of computational evidence suggest no impact on gene product. REVEL score is 0.212 (well below the 0.5 pathogenicity threshold), and BayesDel score is -0.418 (negative, predicting benign). SpliceAI identifies no splicing impact. No HCI prior probability score is available for MBD4.
gene-specific framework lacked a usable explicit final combination framework, so generic ACMG/AMP 2015 final-combination rules were applied as fallback; applied criteria: BA1 stand-alone benign, BS1 strong benign, BS2 strong benign, BP4 supporting benign; combination = 1 stand-alone benign + 2 strong benign + 1 supporting benign, which maps to Benign.
Evidence summaries and captured source records, where available. Missing entries should not be interpreted as negative findings.
gnomAD v4.1: 135,695 / 1,614,010 alleles. Recorded AF 0.0840732. Recorded homozygote count 6177.
This variant is present in gnomAD v2.1 (AF= 0.0788733; MAF= 7.88733%, 22303/282770 alleles, homozygotes = 999) and has highest observed frequency in the Ashkenazi Jewish population (AF= 0.162423; MAF= 16.24228%, 1684/10368 alleles, homozygotes = 131); grpmax FAF= 0.106406.
This variant is present in gnomAD-Canada v1.0 (AF= 0.09180238870792616, 1691/18420 alleles, homozygotes = 90).
No SpliceAI or REVEL score is recorded in the fields used for this tile.
A ClinVar laboratory submission summary was not recorded. ClinVar API review status: criteria provided, multiple submitters, no conflicts.
OncoKB did not identify variant-specific reviewed functional evidence for this variant; gene-level curated context is available for reviewer follow-up. MBD4, a DNA glycosylase, is infrequently altered in cancer.
This variant has previously been reported in somatic cancers (COSMIC; COSV51444644, n = 15 times).
This variant does not lie in a statistically significant hotspot.
ACMG/AMP criteria under Not recorded, with the data and sources behind each one.
26 criteria with recorded statuses: 4 met · 17 not met · 0 not assessed · 5 not applicable. Open any row for the full reasoning, the rule and the evidence behind it.
NM_001276270.2:c.817G>A (p.Ala273Thr) in MBD4 is a common polymorphism present at 7.89–8.41% allele frequency across gnomAD datasets with 999–6,177 homozygous individuals, far exceeding the BA1 stand-alone benign threshold of >1%.
The variant is classified as Benign in ClinVar (Variation ID 1236752) with 2-star review status and five clinical laboratory submissions unanimously agreeing on a benign classification, consistent with the population frequency data.
Multiple in silico predictors support a benign effect: REVEL score 0.212 and BayesDel score -0.418, with no evidence of splicing impact from SpliceAI.
No pathogenic evidence was identified: PVS1 is not applicable to this missense variant; no functional studies (PS3), de novo events (PS2/PM6), segregation data (PP1), or case-control enrichment (PS4) were found.
Based on BA1 alone, this variant meets stand-alone benign criteria. Additional benign evidence from BS1, BS2, and BP4 further supports a benign classification. Classification: BENIGN.
No criteria match.
No further detail was recorded.
Every interpreted variant in MBD4, mapped onto the exon structure of NM_001276270.2. Select a row to find it on the plot.
| Protein | Location | Classification | Link |
|---|
| Ashkenazi Jewish4821 / 29,606 | 0.16404 hom |
| Middle Eastern752 / 6,062 | 0.1265 hom |
| South Asian10157 / 91,076 | 0.11674 hom |
| Remaining individuals5804 / 62,506 | 0.093293 hom |
| European (non-Finnish)100487 / 1,179,954 | 0.0854268 hom |
| African/African American5098 / 75,032 | 0.068180 hom |
| Admixed American3788 / 60,020 | 0.063149 hom |
| East Asian2278 / 44,880 | 0.05181 hom |
| European (Finnish)2482 / 63,962 | 0.03962 hom |
| Amish28 / 912 | 0.0311 hom |
| Ashkenazi Jewish1684 / 10,368 | 0.16131 hom |
| South Asian3352 / 30,612 | 0.11207 hom |
| Remaining individuals686 / 7,224 | 0.09538 hom |
| European (non-Finnish)10731 / 129,128 | 0.083434 hom |
| African/African American1720 / 24,960 | 0.06962 hom |
| East Asian1213 / 19,948 | 0.06140 hom |
| Admixed American1984 / 35,436 | 0.05665 hom |
| European (Finnish)933 / 25,094 | 0.03722 hom |
This variant is present in gnomAD v4.1 (AF= 0.0840732; MAF= 8.40732%, 135695/1614010 alleles, homozygotes = 6177) and has highest observed frequency in the Ashkenazi Jewish population (AF= 0.162839; MAF= 16.28386%, 4821/29606 alleles, homozygotes = 404); grpmax FAF= 0.116705.
This variant is present in gnomAD v2.1 (AF= 0.0788733; MAF= 7.88733%, 22303/282770 alleles, homozygotes = 999) and has highest observed frequency in the Ashkenazi Jewish population (AF= 0.162423; MAF= 16.24228%, 1684/10368 alleles, homozygotes = 131); grpmax FAF= 0.106406.
This variant is present in gnomAD-Canada v1.0 (AF= 0.09180238870792616, 1691/18420 alleles, homozygotes = 90).
REVEL score = 0.212. BayesDel score = -0.417963.
7 paper records listed. No publication is explicitly linked to an applied criterion in the recorded metadata. None of the listed paper records explicitly indicates that the variant is named.
Screenshots represent source records captured during evidence collection. Select one to view the recorded source content.
The evidence statements recorded by the interpretation pipeline. They have not been reinterpreted by the page.
This variant is present in gnomAD v4.1 (AF= 0.0840732; MAF= 8.40732%, 135695/1614010 alleles, homozygotes = 6177) and has highest observed frequency in the Ashkenazi Jewish population (AF= 0.162839; MAF= 16.28386%, 4821/29606 alleles, homozygotes = 404); grpmax FAF= 0.116705.
This variant is present in gnomAD v2.1 (AF= 0.0788733; MAF= 7.88733%, 22303/282770 alleles, homozygotes = 999) and has highest observed frequency in the Ashkenazi Jewish population (AF= 0.162423; MAF= 16.24228%, 1684/10368 alleles, homozygotes = 131); grpmax FAF= 0.106406.
This variant is present in gnomAD-Canada v1.0 (AF= 0.09180238870792616, 1691/18420 alleles, homozygotes = 90).
This variant is present in ClinVar (Variation ID: 1236752); submission details unavailable.
REVEL score = 0.212. BayesDel score = -0.417963.
OncoKB did not identify variant-specific reviewed functional evidence for this variant; gene-level curated context is available for reviewer follow-up. MBD4, a DNA glycosylase, is infrequently altered in cancer.
This variant does not lie in a statistically significant hotspot. This variant has previously been reported in somatic cancers (COSMIC; COSV51444644, n = 15 times).
This variant does not lie in a statistically significant hotspot.